Primary agammaglobulinemia

Primary agammaglobulinemia is a group of hereditary immunodeficiencies characterized by lack of antibodies.

Antibodies are proteins (immunoglobulins) essential for the immune system. B lymphocytes produce them. Antibodies fight against bacteria, viruses, and other foreign substances that threaten the body.

Agammaglobulinemia can also occur on abnormal B lymphocytes. In some forms of primary agammaglobulinemia, neither lymphocyte (T, B) is functioning normally.

There are three clinical forms of primary agammaglobulinemia:

All these diseases are characterized by a weakened immune system that should be strengthened with the administration of gammaglobulins to fight infection.

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